G Kim, N Lee, H Ko, JH Byun, HD Lee, SC Sung, H Kim, KH Choi

Abstract

Cardiac tumours occur rarely in children. We report on the clinical features, echocardiogram and electrocardiographic findings, treatment, and outcomes of primary cardiac tumours in 27 children treated between 2009 and 2017 in our single centre. The most common tumour was rhabdomyoma with tuberous sclerosis in 15 children; two malignant tumours-an angiosarcoma and rhabdomyosarcoma-were also found. Seven patients were haemodynamically unstable: five underwent cardiac surgery, one was managed with everolimus for arrhythmia, and one died of heart failure 1 day after birth despite full medical support. We discuss the various treatment options for haemodynamically unstable paediatric patients with a cardiac tumour.