PMY Tang, KLY Chung, MWY Leung, KKW Liu

Abstract

Introduction: Urethral duplication is a rare congenital anatomical anomaly. It can often be associated with other organ system anomalies. Methods: We report a case of a male child with VACTERAL association and complete duplication of the urethra. The associated congenital anomalies and the various different urethral imaging techniques were also described. Results: The child underwent surgical repair of the duplicated urethra and resection of the associated anterior megalo-urethra at age 6. Early post op follow up showed excellent cosmetic and functional outcome. Discussions: We reviewed the literature regarding the embryology of the male urethra. Classification of the different anatomical variants of urethral duplication and their proposed aetiologies were also discussed.

前言：重複尿道是罕見的先天性解剖異常。它時常伴有其他器官系統異常。方法：我們報導一例有VACTERL聯合徵和完全型重複尿道的男童，並描述相關的先天異常和各種不同的尿道影像技術。結果：此兒童6歲時接受了重複尿道的手術修復和切除相關前部巨尿道。術後早期隨訪顯示了非常好的整形和功能結果。討論：我們回顧了關於男性尿道胚胎學的文獻，並討論了重複尿道的不同解剖變異的分類，及其相關的病因。