Table of Contents

HK J Paediatr (New Series)
Vol 24. No. 3, 2019

HK J Paediatr (New Series) 2019;24:140-146

Original Article

Clinical Manifestations and Outcomes of Cardiac Tumours in Children
兒童心臟腫瘤的臨床表現及預後

G Kim, N Lee, H Ko, JH Byun, HD Lee, SC Sung, H Kim, KH Choi


Abstract

Cardiac tumours occur rarely in children. We report on the clinical features, echocardiogram and electrocardiographic findings, treatment, and outcomes of primary cardiac tumours in 27 children treated between 2009 and 2017 in our single centre. The most common tumour was rhabdomyoma with tuberous sclerosis in 15 children; two malignant tumours-an angiosarcoma and rhabdomyosarcoma-were also found. Seven patients were haemodynamically unstable: five underwent cardiac surgery, one was managed with everolimus for arrhythmia, and one died of heart failure 1 day after birth despite full medical support. We discuss the various treatment options for haemodynamically unstable paediatric patients with a cardiac tumour.

兒童心臟腫瘤是很少見的。我們報告了2009年至2017年在我們單一中心治療的27名兒童原發性心臟腫瘤的臨床特徵、超聲心動圖和心電圖結果、治療方法和結局。最常見的腫瘤為橫紋肌瘤伴結節性硬化症,共15例;另有二例惡性腫瘤──血管肉瘤和橫紋肌肉瘤。7例患者血流動力學不穩定:其中5人接受了心臟手術,另一例需用依維莫司治療心律失常,還有一例儘管給與充分的醫療支援仍在出生後一天死於心力衰竭。我們討論對血液動力學不穩定的兒科心臟腫瘤患者提供不同的治療選擇。

Keyword : Cardiac surgery; Cardiac tumour; Rhabdomyoma

關鍵詞:心外科、心臟腫瘤、橫紋肌瘤

 
 

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